Objective To evaluate the incidence, clinicopathologic features, treatments and prognosis of renal tumor patients under the age of 30 years old. Methods The clinical data of renal tumor patients under 30, who were treated between January 2001 and December 2014, were retrospectively analyzed. The general information, incidence, clinical manifestations, pathological outcomes, treatment strategies, and prognosis were analyzed. Results A total of 137 patients were included in this study, which accounted for 3.84% (137/3570) of all renal tumor cases in our hospital at the same period. The mean age of 137 patients was (24.47±4.80) years old, including 67 males and 70 females. 79 patients (57.66%) were diagnosed during health check-up, 39 patients were diagnosed for abdomen or flank pain, gross hematuria and mass as the main clinical symptoms were separately found in 10 and 7 patients, the other 2 patients saw a doctor for urinary frequency and urgency. 133 patients received operations, the rest received conservative medical management. 125 cases of postoperative pathology were got: 75 renal cell carcinomas, 42 angiomyolipomas, 6 nephroblastomas, one neuroendocrine tumor, and one juxtaglomerular cell tumor. 121 patients had been followed-up. The 3 and 5 years survival rates of renal cell carcinoma were 82.86%(29/35)and 61.53%(8/13). 2 cases of nephroblastoma died of tumor metastasis. All the angiomyolipoma, neuroendocrine tumor, juxtaglomerular cell tumor patients had good prognosis. Conclusion Most of renal tumors in patients under the age of 30 years old are malignant. But it is noteworthy that benign angiomyolipoma also accounts for a considerable proportion. Regular health check-up is benefit for early diagnosis and better prognosis.