【Abstract】Obiective:To discuss the the clinical characteristic and the radiological and pathological features of pulmonary lymphomatoid granulomatosis (LYG). Method：We reviewed the clinical materials of the 1 hospitalized patient with LyG diagnosed by pulmonary biopsy through thoracic surgery，analyzed the results of the clinical manifestation，pathology，diagnosis and the therapy． Results：LyG was a kind of the polysystemic disease，which involved in the lung and skin．Chest Radiology was the main method to detect the disease．Pathology was the key method to the diagnosis．Chemotherapy and radiotherapy were effective． Conclusion：LyG is a T-cell rich B-cell lymphoma which is associated with the immunodeficiency and the infection of EB virus；It is rare in the clinic and is very easily misdiagnosed．