Hepatoblastoma is the most commonly-seen liver tumor in children. The past 30 years has witnessed graduall changes in the diagnosis and treatment of HB: from single operative excision to multimodality therapies. Recently many research groups have focused on the risk groups and stratified treatment, looked for novel potential prognostic risk factors. This paper reviewed the etiology, clinical diagnosis, criterion of risk groups, treatment principle, and prognosis factors of hepatoblastoma in children.