| 摘要: |
| 【摘要】目的 探讨肺淋巴瘤样肉芽肿病的临床、影像及病理学特征，以提高对该病的认识。方法 回顾性分析一例肺淋巴瘤样肉芽肿病G患者的临床、影像、病理学特征及免疫组化学检查特点及治疗。结果 ：肺淋巴瘤样肉芽肿病为多系统疾病，主要累及肺部，其次是皮肤和中枢神经系统。影像学是发现本病的主要手段，病理是确诊的主要依据。部分患者经化、放疗病情缓解。结论：肺淋巴瘤样肉芽肿病是一种与免疫缺陷和EB病毒感染有关的富含T细胞的B细胞淋巴瘤。临床少见，易误诊。 |
| 关键词: 肺淋巴瘤样肉芽肿 淋巴瘤 |
| DOI：10.3724/SP.J.1008.2013.00114 |
| 投稿时间：2012-06-27修订日期：2012-10-18 |
| 基金项目:教育部高等学校博士学科点专项科研基金 (20100072120060),上海市自然科学基金 (10ZR1425000),上海市卫生局重点课题 (2010006),上海市肺科医院课题 (20090018). |
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| Pulmonary lymphomatoid granulomatosis: a case report |
| LIANG Shuo,CAO Wei-jun*,LIU Jin-ming,LI Hui-ping |
(Department of Respiratory Medicine, Shanghai Pulmonary Hospital, Tongji University, Shanghai 200433, China
*Corresponding author.) |
| Abstract: |
| 【Abstract】Obiective:To discuss the the clinical characteristic and the radiological and pathological features of pulmonary lymphomatoid granulomatosis (LYG).
Method：We reviewed the clinical materials of the 1 hospitalized patient with LyG diagnosed by pulmonary biopsy through thoracic surgery，analyzed the results of the clinical manifestation，pathology，diagnosis and the therapy．
Results：LyG was a kind of the polysystemic disease，which involved in the lung and skin．Chest Radiology was the main method to detect the disease．Pathology was the key method to the diagnosis．Chemotherapy and radiotherapy were effective．
Conclusion：LyG is a T-cell rich B-cell lymphoma which is associated with the immunodeficiency and the infection of EB virus；It is rare in the clinic and is very easily misdiagnosed． |
| Key words: pulmonary lymphomatoid granulomatosis lymphoma |
