| 摘要: |
| 目的 总结1例天使综合征（AS）伴中度脊柱侧凸患儿在全身麻醉下行脊柱侧凸后路三维截骨矫形融合内固定术围手术期的护理经验。方法 分析2023年8月4日在我院接受手术治疗的1例AS伴中度脊柱侧凸患儿的临床资料。患儿入院后组建多学科协作团队，查阅相关文献和证据，构建并实施“1＋X”护理方案，方案包括“1”（以脊柱侧凸为核心的围手术期护理要点）和“X”（以AS为核心的若干护理问题和对策）两大方面。结果 患儿手术顺利，术后病情稳定，侧凸畸形明显改善，身高增加7 cm，于术后第10天顺利出院。出院后随访依从性为100%，患儿恢复至术前独立行走状态。结论 AS伴脊柱侧凸“1＋X”护理方案可有效保证围手术期安全，促进患儿康复，同时也为其他罕见病伴脊柱侧凸围手术期护理提供了思路。 |
| 关键词: 天使综合征 脊柱侧凸 癫痫 围手术期护理 |
| DOI：10.16781/j.CN31-2187/R.20240249 |
| 投稿时间：2024-04-17修订日期：2024-12-12 |
| 基金项目: |
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| Perioperative nursing care of a child with Angelman syndrome and moderate scoliosis |
| ZHANG Shanshan,YANG Fang*,GAO Tiantian,SHAO Jie,BAI Yushu,LIU Xuan |
(Department of Spinal Surgery, The First Affiliated Hospital of Naval Medical University (Second Military Medical University), Shanghai 200433, China
*Corresponding author) |
| Abstract: |
| Objective To summarize the perioperative nursing experience of a child with Angelman syndrome (AS) complicated with moderate scoliosis undergoing posterior 3-dimensional osteotomy correction, fusion, and internal fixation under general anesthesia. Methods The clinical data of the child with AS and moderate scoliosis who underwent surgical treatment in our hospital on Aug. 4, 2023, were analyzed. A multidisciplinary team was established upon admission. Relevant literatures and evidences were reviewed to develop and implement a “1＋X” nursing plan, which included 2 components: “1” (core perioperative nursing priorities for scoliosis) and “X” (multiple AS-related nursing issues and corresponding strategies). Results The surgery was successful, with stable postoperative conditions and significant improvement in spinal curvature. The child’s height increased by 7 cm. Discharge occurred on postoperative day 10, with 100% follow-up compliance. The child regained preoperative independent walking ability during follow-up. Conclusion The “1＋X” nursing protocol for AS complicated with scoliosis can effectively ensure perioperative safety and promote recovery, which providing insights for perioperative nursing care of other rare diseases complicated with scoliosis. |
| Key words: Angelman syndrome scoliosis epilepsy perioperative care |
